Related Articles

Lengthy-term survival case of malignant glomus tumor mimicking “dumbbell-shaped” neurogenic tumor.

Eur Backbone J. 2017 Might;26(Suppl 1):42-46

Authors: Nagata Ok, Hashizume H, Yamada H, Yoshida M

Summary
PURPOSE: We report a really uncommon case of long-term survival case of malignant glomus tumor (MGT) with out widespread metastasis.
STUDY PARTICIPANTS: Sixty-three-year-old lady who skilled a number of relapses over a 40-year interval starting with a scapular lesion since she was at age 21.
RESULTS: After 4 native recurrences, the affected person underwent extensive resection of the scapula at age 36. 13 years later, the affected person had a neck tumor on the similar facet with the scapulectomy. The tumor was originated from the C6 spinal nerve and was resected. Twelve years after the surgical procedure, the cervical tumor relapsed with myelopathy at age 61. The tumor infiltrated from the extraspinal canal to the intraspinal canal on the C5/C6 foramen and appeared as a dumbbell-like tumor. Moreover, the native recurrence occurred 2 years after the operation at age 63. The tumors that had been detected at age 36 and age 63 had been confirmed to be histologically equivalent. These had been greater than 2 cm in measurement and arose from a deep location. The basement membrane stained positively for collagen kind IV and ?-smooth muscle actin on immunohistochemistry. Primarily based on these features, the tumor was identified as an MGT.
CONCLUSIONS: That is the primary case report of MGT which lesions at two time factors had been confirmed to have frequent histological options and which confirmed the long-term survival over a 40-year interval.

PMID: 27421277 [PubMed – indexed for MEDLINE]