Occipitoatlantoaxial rotatory fixation (OAARF) is a rare condition involving fixed rotational subluxation of the atlas in relation to both the occiput and axis. Atlantoaxial rotatory fixation (AARF) appears to precede OAARF in most cases, as untreated AARF may cause compensatory counter-rotation and occipitoaxial fixation at an apparently neutral head position. We report a case of OAARF in an 8-year-old girl with juvenile idiopathic arthritis. Cervical imaging demonstrated slight rightward rotation of the occiput at 7.63 degrees in relation to C-2 and significant rightward rotation of C-1 at 65.90 degrees in relation to the occiput and at 73.53 degrees in relation to C-2. An attempt at closed reduction with halo traction was unsuccessful. Definitive treatment included open reduction, C-1 laminectomy, and occipitocervical internal fixation and fusion
Keywords : Arthritis,Juvenile,Atlanto-Axial Joint,Child,complications,diagnostic imaging,etiology,Female,Head,Humans,Imaging,Three-Dimensional,Joint Instability,Laminectomy,methods,Neurosurgery,Occipital Bone,Radiography,Range of Motion,Articular,Rotation,Spinal Fusion,surgery,Traction,, Occipitoatlantoaxial,Rotatory,Fixation, ct scan spine cervical
Date of Publication : 2011 Aug
Authors : Fusco MR;Hankinson TC;Rozzelle CJ;
Organisation : Division of Pediatric Neurosurgery, Children’s Hospital of Alabama, Birmingham, Alabama, USA. fusco@ccc.uab.edu
Journal of Publication : J Neurosurg Pediatr
Pubmed Link : https://www.ncbi.nlm.nih.gov/pubmed/21806363
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